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Pulmonary arteriovenous malformations

Pulmonary arteriovenous malformations (PAVMs) are most commonly seen in association with Osler-Weber-Rendu syndrome—hereditary haemorrhagic telangiectasia. This is an autosomal dominant vascular dysplasia characterized by epistaxis, mucocutaneous telangiectasias, and arteriovenous malformations in the brain, lung, liver, gastrointestinal tract, or spine.

The risks included bleeding leading to potentially catastrophic haemoptysis, infectious and ischaemic neurological manifestations due to para­doxical emboli, and high-output cardiac failure due to systemic ar­teriovenous shunting.

Those with PAVMs that bleed in pregnancy should be treated as outside pregnancy with coiling of the PAVMs using interventional radiology. Women should therefore deliver in facilities with inter­ventional radiology support.

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Source: Arulkumaran S., Ledger W., Denny L., Doumouchtsis S. (eds.). Oxford Textbook of Obstetrics and Gynaecology. Oxford University Press,2020. — 928 p.. 2020
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