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Coagulative Disorders in HIV-Infect­ed Patients Leading to Microvascular Risk of Thrombosis

Microthrombotic Disease in HIVPatients

Thrombotic thrombocytopenic purpura (TTP) is a microthrombotic disease of rare occurrence. The most clinically sensitive microcirculations to TTP are those of the brain, kidney, and liver, explaining the most frequent clinical manifestations of the dis­ease.

One of the main pathogenic mecha­nism of TTP is a deficiency (hereditary or acquired) of an endogenous metallopro­tease (ADAMS 13) which physiologically degrades the highest-molecular-weight forms of VWF into lower-molecular-weight fragments. The increased concentration of higher-molecular-weight forms of VWF trig­gers in vivo platelet aggregation and forma­tion of platelet microthrombi, which plug the microcirculations of the most sensitive organs. The treatment is based on plasma exchange and infusion of fresh frozen plas­ma to remove the highest-molecular-weight forms of VWF, to remove the inhibitors of ADAMS 13, and to replenish ADAMS 13. From an epidemiologic point of view, TTP in HIV infection is associated with opportunis­tic infections (cryptosporidiosis, cytomega lovirus infection) [54], with HIV-associated malignancies, or with HIV-associated wast­ing syndrome. The incidence of TTP is sig­nificantly reduced after the introduction of HAART (Fig. 4) [55, 56].

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Source: Barbaro Giuseppe, Boccara Franc (eds.). Cardiovascular Disease in AIDS. 2nd edition. — Springer,2009. — 169 p.. 2009
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